- Case Report
- Two Cases of Congenital Hepatic Fibrosis
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Cue Jung Hwang, Young Hun Kim, Dae Kyun Koh, Byung Churl Lee
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Clin Exp Pediatr. 1992;35(4):569-574. Published online April 15, 1992
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The congenital hepatic fibrosis is a rare condition defined pathologically by the presence within the line of bands of fibrous tissue which after contain linear or circular spaces lined by bile duct cells, It is commonly associated with intrahepatic portal hypertension but hepatocellular function is almost always preserved. The prinicipal clinical features of this disease are abdominal distension, firm hepatomegaly,... |
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